Autoimmune inner ear disease (AIED)

Autoimmune inner ear disease (AIED) is an unusual form of progressive non-age-related sensorineural hearing loss and sometimes vertigo. It occurs in both ears with cochlear and vestibular symptoms that progress over a period of weeks to months and affects hearing, and often balance function, in both ears. The classic presentation is with bilateral fluctuating but progressive sensorineural hearing loss leading on to severe deafness. Tinnitus (ringing, tinkling, buzzing, or other sounds in the ear) and intra-aural pressure may occur, as well as dizziness or vertigo.